Atypical Presentation of Extranodal Rosai-Dorfman Disease

Brandon L. Prendes, William T. Brinkman, Anita L. Sengupta, Joseph E. Bavaria

Research output: Contribution to journalArticle

7 Scopus citations

Abstract

We describe a 42-year-old woman with progressive dyspnea on exertion resulting from pulmonary artery compression by a mediastinal mass due to extranodal Rosai-Dorfman disease. After initial biopsies were inconclusive, she underwent surgical resection of the mass to relieve the pulmonary artery compression, which was causing severe right ventricular dysfunction. Debulking of the mass required resection and reconstruction of the ascending aorta, pulmonary trunk, and bilateral pulmonary arteries using cardiopulmonary bypass and circulatory arrest. We believe this is the first report of Rosai-Dorfman disease manifesting as compression of the thoracic great vessels.

Original languageEnglish (US)
Pages (from-to)616-618
Number of pages3
JournalAnnals of Thoracic Surgery
Volume87
Issue number2
DOIs
Publication statusPublished - Feb 2009

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ASJC Scopus subject areas

  • Cardiology and Cardiovascular Medicine
  • Surgery
  • Pulmonary and Respiratory Medicine

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