Benign sacrococcygeal neoplasm arising at birth from a giant congenital melanocytic nevus

Jason A. Snyder, Nini Khozeimeh, Christine Reyes, Faisal G. Qureshi

Research output: Contribution to journalReview article

1 Citation (Scopus)

Abstract

Giant congenital melanocytic nevi (CMN) are considered to be premalignant with the highest risk for conversion to melanoma. Solid tumors within giant CMN presenting at birth are relatively unusual, and a variety of malignancies have been reported within these masses. However, the frequency of malignancy in these tumors is unknown. We report the unusual case of a female neonate who was born with 2 large, perianal masses within a giant CMN over her trunk. We resected the larger of the 2 masses because of discomfort and bleeding. The mass consisted of an outgrowth of melanocytes with benign characteristics. The smaller of the 2 masses was managed expectantly and has subsequently decreased in size. We propose that pathologically benign masses within giant CMNs may not require immediate resection. We will discuss the management and pathologic findings of this case and review the literature regarding management of CMN-associated neoplasms arising at birth.

Original languageEnglish (US)
Pages (from-to)408-411
Number of pages4
JournalJournal of Pediatric Surgery
Volume47
Issue number2
DOIs
StatePublished - Feb 1 2012

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Pigmented Nevus
Parturition
Neoplasms
Melanocytes
Melanoma
Hemorrhage

Keywords

  • Benign neoplasm
  • Congenital giant nevus
  • Congenital melanocytic nevus
  • Perianal neoplasm
  • Sacrococcygeal neoplasm

ASJC Scopus subject areas

  • Surgery
  • Pediatrics, Perinatology, and Child Health

Cite this

Benign sacrococcygeal neoplasm arising at birth from a giant congenital melanocytic nevus. / Snyder, Jason A.; Khozeimeh, Nini; Reyes, Christine; Qureshi, Faisal G.

In: Journal of Pediatric Surgery, Vol. 47, No. 2, 01.02.2012, p. 408-411.

Research output: Contribution to journalReview article

Snyder, Jason A. ; Khozeimeh, Nini ; Reyes, Christine ; Qureshi, Faisal G. / Benign sacrococcygeal neoplasm arising at birth from a giant congenital melanocytic nevus. In: Journal of Pediatric Surgery. 2012 ; Vol. 47, No. 2. pp. 408-411.
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