TY - JOUR
T1 - Congenital corrected transposition with atrial inversion and normal hemodynamics
AU - Fixler, David E
PY - 1971/3
Y1 - 1971/3
N2 - The first reported case of corrected transposition with atrial inversion and normal hemodynamics is presented. The patient is an asymptomatic 10-year-old boy with a loud single second heart sound and a soft systolic ejection murmur at the base. The electrocardiogram reveals a P-wave vector directed to the right and inferiorly, suggesting atrial inversion. The presence of q waves in V4-6 suggests noninverted ventricles. Chest roentgenograms show dextrocardia, situs inversus, and a right aortic arch. Cardiac catheterization hemodynamic data reveal no evidence of a shunt or significant valvar abnormalities. On angiography the aortic valve lies to the right of the pulmonic valve and is more cephalad indicating D-transposition of the great arteries. The circulation is functionally completely corrected, since the systemic venous drainage enters the left-sided atrium and is ejected into the pulmonary artery by the left ventricle. The pulmonary venous drainage enters the right-sided atrium and is ejected into the transposed aorta by the right ventricle. A systematic approach to chamber localization is reviewed based upon: (1) the relationship of the viscera and atria (visceral atrial situs); (2) the relationship of the ventricles (type of bulboventricular loop); (3) the relationship of the great arteries.
AB - The first reported case of corrected transposition with atrial inversion and normal hemodynamics is presented. The patient is an asymptomatic 10-year-old boy with a loud single second heart sound and a soft systolic ejection murmur at the base. The electrocardiogram reveals a P-wave vector directed to the right and inferiorly, suggesting atrial inversion. The presence of q waves in V4-6 suggests noninverted ventricles. Chest roentgenograms show dextrocardia, situs inversus, and a right aortic arch. Cardiac catheterization hemodynamic data reveal no evidence of a shunt or significant valvar abnormalities. On angiography the aortic valve lies to the right of the pulmonic valve and is more cephalad indicating D-transposition of the great arteries. The circulation is functionally completely corrected, since the systemic venous drainage enters the left-sided atrium and is ejected into the pulmonary artery by the left ventricle. The pulmonary venous drainage enters the right-sided atrium and is ejected into the transposed aorta by the right ventricle. A systematic approach to chamber localization is reviewed based upon: (1) the relationship of the viscera and atria (visceral atrial situs); (2) the relationship of the ventricles (type of bulboventricular loop); (3) the relationship of the great arteries.
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U2 - 10.1016/0002-8703(71)90109-8
DO - 10.1016/0002-8703(71)90109-8
M3 - Article
C2 - 5547438
AN - SCOPUS:0015029421
SN - 0002-8703
VL - 81
SP - 387
EP - 391
JO - American heart journal
JF - American heart journal
IS - 3
ER -