Focal fibrocartilaginous dysplasia in the upper extremity

Todd L. Lincoln, John G. Birch

Research output: Contribution to journalArticlepeer-review

29 Scopus citations

Abstract

Focal fibrocartilaginous dysplasia is a benign lesion known to cause tibia vara in young children. To date, this lesion has been recognized in only the proximal medial tibia. This study reports two additional cases of focal fibrocartilaginous dysplasia occurring in the long bones of the upper extremity. The clinical presentation, radiographic appearance, histopathology, and natural history of focal fibrocartilaginous dysplasia in the humerus and ulna are analogous to published descriptions involving the tibia. Spontaneous resolution of the lesion and the resultant angular deformity is possible but not entirely predictable. Limb-length discrepancy should be anticipated.

Original languageEnglish (US)
Pages (from-to)528-532
Number of pages5
JournalJournal of Pediatric Orthopaedics
Volume17
Issue number4
DOIs
StatePublished - Jul 1997

Keywords

  • Focal fibrocartilaginous dysplasia
  • Humerus
  • Tibia vara
  • Ulna

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health
  • Orthopedics and Sports Medicine

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