Implantable defibrillators in long QT syndrome, brugada syndrome, hypertrophic cardiomyopathy, and arrhythmogenic right ventricular cardiomyopathy

Mustafa Dohadwala, Mark S. Link

Research output: Contribution to journalReview article

3 Scopus citations


Sudden death is often the first manifestation in inherited cardiac arrhythmia syndromes. Patients with long QT syndrome who have an episode of syncope while on beta-blockade should be offered an implantable cardioverter-defibrillator (ICD). In Brugada syndrome and hypertrophic cardiomyopathy, ICDs are often the most effective treatment of primary and secondary prevention of cardiac arrest. Risk stratification is crucial in identifying those at greatest risk to provide lifesaving therapy with an ICD while avoiding complications in those unlikely to receive benefit.

Original languageEnglish (US)
Pages (from-to)305-318
Number of pages14
JournalCardiology Clinics
Issue number2
Publication statusPublished - Jan 1 2014



  • Arrhythmogenic right ventricular cardiomyopathy
  • Brugada syndrome
  • Channelopathy
  • Genetic syndrome
  • Hypertrophic cardiomyopathy
  • Long QT syndrome
  • Sudden death

ASJC Scopus subject areas

  • Cardiology and Cardiovascular Medicine
  • Medicine(all)

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