Meconium ileus in Cystic Fibrosis

Meghana Sathe, Roderick Houwen

Research output: Contribution to journalArticlepeer-review

85 Scopus citations

Abstract

Meconium ileus (MI) is often the first manifestation of cystic fibrosis (CF) and occurs in approximately 20% of patients diagnosed with CF. This article reviews the pathophysiology of MI and its clinical presentation. It focuses on the medical and surgical management emphasizing the importance of nutrition and a multidisciplinary approach to improve both short-term and long-term outcomes for CF patients with MI.

Original languageEnglish (US)
Pages (from-to)S32-S39
JournalJournal of Cystic Fibrosis
Volume16
DOIs
StatePublished - Nov 2017

Keywords

  • Cystic fibrosis
  • Gastrografin
  • Meconium ileus
  • Meconium peritonitis

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health
  • Pulmonary and Respiratory Medicine

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