Moyamoya syndrome as an unusual presenting manifestation of systemic lupus erythematosus in a young woman

Guanen Zhou, Zhongping An, Sankalp Gokhale

Research output: Contribution to journalArticle

4 Citations (Scopus)

Abstract

Objective: To describe a rare case of moyamoya syndrome associated with systemic lupus erythematosus (SLE).Presentation and Intervention: A 22-year-old woman presented with left-sided hemiparesis in addition to fever, fatigue and malar rash. Brain magnetic resonance imaging revealed acute infarction in the right middle cerebral artery territory. Cerebral angiography showed features of moyamoya syndrome. Brain biopsy showed evidence of vasculitis. She responded well to steroid therapy. Conclusion: This case represented a rare co-occurrence of SLE-related vasculitis and moyamoya syndrome. Early vascular imaging is critical in patients with SLE and suspected ischemic stroke.

Original languageEnglish (US)
Pages (from-to)279-281
Number of pages3
JournalMedical Principles and Practice
Volume23
Issue number3
DOIs
StatePublished - 2014

Fingerprint

Moyamoya Disease
Systemic Lupus Erythematosus
Vasculitis
Cerebral Angiography
Middle Cerebral Artery Infarction
Brain
Paresis
Exanthema
Fatigue
Blood Vessels
Fever
Stroke
Steroids
Magnetic Resonance Imaging
Biopsy
Therapeutics

Keywords

  • Angiography
  • Ischemic stroke
  • Moyamoya syndrome
  • Systemic lupus erythematosus

ASJC Scopus subject areas

  • Medicine(all)

Cite this

Moyamoya syndrome as an unusual presenting manifestation of systemic lupus erythematosus in a young woman. / Zhou, Guanen; An, Zhongping; Gokhale, Sankalp.

In: Medical Principles and Practice, Vol. 23, No. 3, 2014, p. 279-281.

Research output: Contribution to journalArticle

@article{30586bdd04874eb68e4ebf455992a292,
title = "Moyamoya syndrome as an unusual presenting manifestation of systemic lupus erythematosus in a young woman",
abstract = "Objective: To describe a rare case of moyamoya syndrome associated with systemic lupus erythematosus (SLE).Presentation and Intervention: A 22-year-old woman presented with left-sided hemiparesis in addition to fever, fatigue and malar rash. Brain magnetic resonance imaging revealed acute infarction in the right middle cerebral artery territory. Cerebral angiography showed features of moyamoya syndrome. Brain biopsy showed evidence of vasculitis. She responded well to steroid therapy. Conclusion: This case represented a rare co-occurrence of SLE-related vasculitis and moyamoya syndrome. Early vascular imaging is critical in patients with SLE and suspected ischemic stroke.",
keywords = "Angiography, Ischemic stroke, Moyamoya syndrome, Systemic lupus erythematosus",
author = "Guanen Zhou and Zhongping An and Sankalp Gokhale",
year = "2014",
doi = "10.1159/000354109",
language = "English (US)",
volume = "23",
pages = "279--281",
journal = "Medical Principles and Practice",
issn = "1011-7571",
publisher = "S. Karger AG",
number = "3",

}

TY - JOUR

T1 - Moyamoya syndrome as an unusual presenting manifestation of systemic lupus erythematosus in a young woman

AU - Zhou, Guanen

AU - An, Zhongping

AU - Gokhale, Sankalp

PY - 2014

Y1 - 2014

N2 - Objective: To describe a rare case of moyamoya syndrome associated with systemic lupus erythematosus (SLE).Presentation and Intervention: A 22-year-old woman presented with left-sided hemiparesis in addition to fever, fatigue and malar rash. Brain magnetic resonance imaging revealed acute infarction in the right middle cerebral artery territory. Cerebral angiography showed features of moyamoya syndrome. Brain biopsy showed evidence of vasculitis. She responded well to steroid therapy. Conclusion: This case represented a rare co-occurrence of SLE-related vasculitis and moyamoya syndrome. Early vascular imaging is critical in patients with SLE and suspected ischemic stroke.

AB - Objective: To describe a rare case of moyamoya syndrome associated with systemic lupus erythematosus (SLE).Presentation and Intervention: A 22-year-old woman presented with left-sided hemiparesis in addition to fever, fatigue and malar rash. Brain magnetic resonance imaging revealed acute infarction in the right middle cerebral artery territory. Cerebral angiography showed features of moyamoya syndrome. Brain biopsy showed evidence of vasculitis. She responded well to steroid therapy. Conclusion: This case represented a rare co-occurrence of SLE-related vasculitis and moyamoya syndrome. Early vascular imaging is critical in patients with SLE and suspected ischemic stroke.

KW - Angiography

KW - Ischemic stroke

KW - Moyamoya syndrome

KW - Systemic lupus erythematosus

UR - http://www.scopus.com/inward/record.url?scp=84901416036&partnerID=8YFLogxK

UR - http://www.scopus.com/inward/citedby.url?scp=84901416036&partnerID=8YFLogxK

U2 - 10.1159/000354109

DO - 10.1159/000354109

M3 - Article

VL - 23

SP - 279

EP - 281

JO - Medical Principles and Practice

JF - Medical Principles and Practice

SN - 1011-7571

IS - 3

ER -