Moyamoya syndrome as an unusual presenting manifestation of systemic lupus erythematosus in a young woman

Guanen Zhou, Zhongping An, Sankalp Gokhale

Research output: Contribution to journalArticlepeer-review

14 Scopus citations

Abstract

Objective: To describe a rare case of moyamoya syndrome associated with systemic lupus erythematosus (SLE).Presentation and Intervention: A 22-year-old woman presented with left-sided hemiparesis in addition to fever, fatigue and malar rash. Brain magnetic resonance imaging revealed acute infarction in the right middle cerebral artery territory. Cerebral angiography showed features of moyamoya syndrome. Brain biopsy showed evidence of vasculitis. She responded well to steroid therapy. Conclusion: This case represented a rare co-occurrence of SLE-related vasculitis and moyamoya syndrome. Early vascular imaging is critical in patients with SLE and suspected ischemic stroke.

Original languageEnglish (US)
Pages (from-to)279-281
Number of pages3
JournalMedical Principles and Practice
Volume23
Issue number3
DOIs
StatePublished - May 2014

Keywords

  • Angiography
  • Ischemic stroke
  • Moyamoya syndrome
  • Systemic lupus erythematosus

ASJC Scopus subject areas

  • General Medicine

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