Native atrial septal restriction after Fontan palliation successfully treated with transcatheter Diabolo stent

Osamah Aldoss, Benjamin E. Reinking, Abhay Divekar

Research output: Contribution to journalArticlepeer-review

2 Scopus citations

Abstract

A 6-year-old male child born with hypoplastic left heart syndrome (HLHS) was palliated with an extracardiac nonfenestrated Fontan procedure (18-mm Gore-Tex tube graft). He developed low-pressure (mean Fontan pressure 10 mmHg) protein-losing enteropathy 6 months after Fontan palliation. After initially responding to medical therapy and transcatheter pulmonary artery stent implantation, he developed medically refractory protein-losing enteropathy. At this time, his transthoracic echocardiogram showed new restriction across his native atrial septum with an 8 mmHg mean gradient. Cardiac catheterization now showed high-pressure (mean Fontan pressure 18-20 mmHg) protein-losing enteropathy and a new 6 mmHg mean gradient across the atrial septum. To avoid cardiopulmonary bypass, he underwent successful transcatheter relief of atrial septal restriction and creation of a fenestration with rapid clinical and biochemical improvement of his protein-losing enteropathy.

Original languageEnglish (US)
Pages (from-to)49-52
Number of pages4
JournalAnnals of Pediatric Cardiology
Volume9
Issue number1
DOIs
StatePublished - Jan 1 2016
Externally publishedYes

Keywords

  • atrial septal restriction
  • Diabolo stent
  • hypoplastic left heart syndrome (HLHS)

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health
  • Cardiology and Cardiovascular Medicine

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