TY - JOUR
T1 - Persistent fetal vasculature presenting with axial elongation and platyphakia
AU - Lin, James
AU - Paez-Escamilla, Manuel
AU - Teira, Laila E.
AU - Fallas, Brenda
AU - Harbour, J. William
N1 - Publisher Copyright:
© 2018 American Association for Pediatric Ophthalmology and Strabismus
PY - 2019/2
Y1 - 2019/2
N2 - Leukocoria in children should always raise the concern for retinoblastoma. However, a variety of non-neoplastic conditions can also present with leukocoria, including persistent fetal vasculature (PFV), a nonhereditary, congenital anomaly caused by a failure of the fetal intraocular vasculature to regress during development. Classically PFV presents with features that make it easily distinguishable from retinoblastoma, including microphthalmia, retrolental fibrovascular membrane, central dragging of ciliary processes, and cataract. We present an atypical case of PFV in a 9-month-old boy who presented with the unusual features of axial myopia and platyphakia.
AB - Leukocoria in children should always raise the concern for retinoblastoma. However, a variety of non-neoplastic conditions can also present with leukocoria, including persistent fetal vasculature (PFV), a nonhereditary, congenital anomaly caused by a failure of the fetal intraocular vasculature to regress during development. Classically PFV presents with features that make it easily distinguishable from retinoblastoma, including microphthalmia, retrolental fibrovascular membrane, central dragging of ciliary processes, and cataract. We present an atypical case of PFV in a 9-month-old boy who presented with the unusual features of axial myopia and platyphakia.
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U2 - 10.1016/j.jaapos.2018.06.005
DO - 10.1016/j.jaapos.2018.06.005
M3 - Article
C2 - 30176292
AN - SCOPUS:85053913727
SN - 1091-8531
VL - 23
SP - 51
EP - 53
JO - Journal of AAPOS
JF - Journal of AAPOS
IS - 1
ER -