Primary pulmonary hypertension: An unusual case associated with extrahepatic portal hypertension

M. D. Cohen, L. J. Rubin, W. E. Taylor, J. A. Cuthbert

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47 Scopus citations


A patient with both extrahepatic portal hypertension and primary pulmonary hypertension is reported. The pulmonary hypertension developed without a surgical portal-systemic shunt, and at autopsy there was no evidence of a large spontaneous shunt. This association of pulmonary arterial hypertension and portal venous hypertension without either intrinsic liver disease or a large portal-systemic anastomosis has not been reported previously. Our case supports the concept that portal hypertension with its attendant portal-systemic collateral circulation may be the major predisposing cause of pulmonary hypertension both in intrinsic liver disease and extrahepatic portal vein obstruction.

Original languageEnglish (US)
Pages (from-to)588-592
Number of pages5
Issue number4
Publication statusPublished - 1983


ASJC Scopus subject areas

  • Hepatology

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