Primary systemic amyloidosis presenting with advanced heart failure

Sameer K. Mehta, John Cogan, Sharon C Reimold, James A de Lemos

Research output: Contribution to journalArticle

6 Citations (Scopus)

Abstract

Primary systemic amyloidosis (AL) is a rare, sporadic disease caused by deposition of immunoglobulin light chains in various tissues; symptoms vary based on which organs are infiltrated by the amyloid fibrils. Cardiac involvement occurs in up to 50% of patients with primary amyloidosis and is associated with a very poor prognosis. We report a case of a 57-year-old black man who presented with symptoms consistent with congestive heart failure. He was later found to have primary systemic amyloidosis, confirmed by abdominal fat pad biopsy.

Original languageEnglish (US)
Pages (from-to)152-155
Number of pages4
JournalCardiology in Review
Volume11
Issue number3
DOIs
StatePublished - May 2003

Fingerprint

Heart Failure
Immunoglobulin Light Chains
Abdominal Fat
Rare Diseases
Amyloid
Adipose Tissue
Biopsy
Primary amyloidosis

Keywords

  • Congestive heart failure
  • Systemic amyloidosis

ASJC Scopus subject areas

  • Cardiology and Cardiovascular Medicine

Cite this

Primary systemic amyloidosis presenting with advanced heart failure. / Mehta, Sameer K.; Cogan, John; Reimold, Sharon C; de Lemos, James A.

In: Cardiology in Review, Vol. 11, No. 3, 05.2003, p. 152-155.

Research output: Contribution to journalArticle

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