"Proximal-type" and classic epithelioid sarcomas represent a clinicopathologic continuum: Case report

Dinesh Rakheja, Kathleen S Wilson, John Meehan, Roger A. Schultz, Ana M. Gomez

Research output: Contribution to journalArticle

17 Scopus citations


We report a case of an epithelioid sarcoma that occurred in the right hand of a 14-year-old boy and had the "proximal-type" morphology and a complex, near-tetraploid karyotype. The tumor metastasized to the lungs, where the morphology was typical for the classic epithelioid sarcoma. Based on the morphologic and cytogenetic findings in this case, we suggest that the proximal-type and the classic epithelioid sarcomas are not distinct entities but represent a continuum.

Original languageEnglish (US)
Pages (from-to)105-114
Number of pages10
JournalPediatric and Developmental Pathology
Issue number1
StatePublished - Feb 1 2005



  • Cytogenetics
  • Epithelioid sarcoma
  • Proximal-type epithelioid sarcoma

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health
  • Pathology and Forensic Medicine

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