Staged male urethroplasty transferring megalourethra tissue as free graft dorsal inlay to proximal urethral atresia in VACTERL association

Research output: Contribution to journalArticle

2 Citations (Scopus)

Abstract

Megalourethra is a rare spectrum of urologic malformations of penile corporal structures frequently associated with multiple congenital anomalies, such as prune belly syndrome or vertebral, anorectal, cardiac, trachea-esophageal, renal, and limb (VACTERL association) defects. A 6-year-old boy with VACTERL association and proximal urethral atresia with distal fusiform megalourethra underwent staged reconstruction, including appendicovesicostomy, perineal urethrostomy, and first-stage urethroplasty with a dorsal inlay free graft of megalourethra tissue to the proximal urethral atretic region, followed by second-stage urethroplasty. At 2.6 years of follow-up, he was continent, voids per urethra without postvoid residual urine volume, and no longer performs clean intermittent catheterization by way of the appendicovesicostomy.

Original languageEnglish (US)
Pages (from-to)1417-1419
Number of pages3
JournalUrology
Volume78
Issue number6
DOIs
StatePublished - Dec 2011

Fingerprint

Inlays
Prune Belly Syndrome
Intermittent Urethral Catheterization
Transplants
Residual Volume
Urethra
Trachea
Extremities
Urine
Kidney
VACTERL association

ASJC Scopus subject areas

  • Urology

Cite this

@article{e536dd3341174f2fbfbad1fc46713830,
title = "Staged male urethroplasty transferring megalourethra tissue as free graft dorsal inlay to proximal urethral atresia in VACTERL association",
abstract = "Megalourethra is a rare spectrum of urologic malformations of penile corporal structures frequently associated with multiple congenital anomalies, such as prune belly syndrome or vertebral, anorectal, cardiac, trachea-esophageal, renal, and limb (VACTERL association) defects. A 6-year-old boy with VACTERL association and proximal urethral atresia with distal fusiform megalourethra underwent staged reconstruction, including appendicovesicostomy, perineal urethrostomy, and first-stage urethroplasty with a dorsal inlay free graft of megalourethra tissue to the proximal urethral atretic region, followed by second-stage urethroplasty. At 2.6 years of follow-up, he was continent, voids per urethra without postvoid residual urine volume, and no longer performs clean intermittent catheterization by way of the appendicovesicostomy.",
author = "Aditya Bagrodia and Selcuk Yucel and Baker, {Linda A.}",
year = "2011",
month = "12",
doi = "10.1016/j.urology.2011.03.023",
language = "English (US)",
volume = "78",
pages = "1417--1419",
journal = "Urology",
issn = "0090-4295",
publisher = "Elsevier Inc.",
number = "6",

}

TY - JOUR

T1 - Staged male urethroplasty transferring megalourethra tissue as free graft dorsal inlay to proximal urethral atresia in VACTERL association

AU - Bagrodia, Aditya

AU - Yucel, Selcuk

AU - Baker, Linda A.

PY - 2011/12

Y1 - 2011/12

N2 - Megalourethra is a rare spectrum of urologic malformations of penile corporal structures frequently associated with multiple congenital anomalies, such as prune belly syndrome or vertebral, anorectal, cardiac, trachea-esophageal, renal, and limb (VACTERL association) defects. A 6-year-old boy with VACTERL association and proximal urethral atresia with distal fusiform megalourethra underwent staged reconstruction, including appendicovesicostomy, perineal urethrostomy, and first-stage urethroplasty with a dorsal inlay free graft of megalourethra tissue to the proximal urethral atretic region, followed by second-stage urethroplasty. At 2.6 years of follow-up, he was continent, voids per urethra without postvoid residual urine volume, and no longer performs clean intermittent catheterization by way of the appendicovesicostomy.

AB - Megalourethra is a rare spectrum of urologic malformations of penile corporal structures frequently associated with multiple congenital anomalies, such as prune belly syndrome or vertebral, anorectal, cardiac, trachea-esophageal, renal, and limb (VACTERL association) defects. A 6-year-old boy with VACTERL association and proximal urethral atresia with distal fusiform megalourethra underwent staged reconstruction, including appendicovesicostomy, perineal urethrostomy, and first-stage urethroplasty with a dorsal inlay free graft of megalourethra tissue to the proximal urethral atretic region, followed by second-stage urethroplasty. At 2.6 years of follow-up, he was continent, voids per urethra without postvoid residual urine volume, and no longer performs clean intermittent catheterization by way of the appendicovesicostomy.

UR - http://www.scopus.com/inward/record.url?scp=82955249232&partnerID=8YFLogxK

UR - http://www.scopus.com/inward/citedby.url?scp=82955249232&partnerID=8YFLogxK

U2 - 10.1016/j.urology.2011.03.023

DO - 10.1016/j.urology.2011.03.023

M3 - Article

C2 - 21601242

AN - SCOPUS:82955249232

VL - 78

SP - 1417

EP - 1419

JO - Urology

JF - Urology

SN - 0090-4295

IS - 6

ER -