Surgical Reconstruction for Severe Tracheal Obstruction in Morquio A Syndrome

Christian Pizarro, Ryan R Davies, Mary Theroux, Ellen A. Spurrier, Lauren W. Averill, Shunji Tomatsu

Research output: Contribution to journalArticle

14 Citations (Scopus)

Abstract

Progressive tracheal obstruction is commonly seen in Morquio A syndrome and can lead to life-threatening complications. Although tracheostomy can address severe upper airway obstruction, lower airway obstruction, commonly associated with a narrow thoracic inlet and vascular compression, requires an alternative approach. We describe the case of a 16-year-old patient with Morquio A syndrome whose near-fatal tracheal obstruction was relieved by timely surgical tracheal vascular reconstruction with dramatic resolution of his respiratory symptoms.

Original languageEnglish (US)
Pages (from-to)e329-e331
JournalAnnals of Thoracic Surgery
Volume102
Issue number4
DOIs
StatePublished - Oct 1 2016

Fingerprint

Mucopolysaccharidosis IV
Airway Obstruction
Blood Vessels
Tracheostomy
Thorax

ASJC Scopus subject areas

  • Surgery
  • Pulmonary and Respiratory Medicine
  • Cardiology and Cardiovascular Medicine

Cite this

Surgical Reconstruction for Severe Tracheal Obstruction in Morquio A Syndrome. / Pizarro, Christian; Davies, Ryan R; Theroux, Mary; Spurrier, Ellen A.; Averill, Lauren W.; Tomatsu, Shunji.

In: Annals of Thoracic Surgery, Vol. 102, No. 4, 01.10.2016, p. e329-e331.

Research output: Contribution to journalArticle

Pizarro, Christian ; Davies, Ryan R ; Theroux, Mary ; Spurrier, Ellen A. ; Averill, Lauren W. ; Tomatsu, Shunji. / Surgical Reconstruction for Severe Tracheal Obstruction in Morquio A Syndrome. In: Annals of Thoracic Surgery. 2016 ; Vol. 102, No. 4. pp. e329-e331.
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