Surgical resection of giant fibrous dysplasia for near respiratory collapse

Jennifer L. Dixon, W. Roy Smythe, Philip A. Rascoe, Scott I. Reznik

Research output: Contribution to journalArticlepeer-review

2 Scopus citations

Abstract

Fibrous dysplasia may involve the ribs or thoracic spine and cause progressive asphyxiation. We present a 41-year-old man with polyostotic fibrous dysplasia who was admitted to the hospital with progressive shortness of breath requiring initiation of supplemental oxygen. Pulmonary function test results revealed severely limited function with forced expiratory volume in 1 second (FEV1) of 14% predicted and diffusion capacity of 17%. As a lifesaving effort, the patient was offered resection, decortication, and chest wall reconstruction, after which the lung reexpanded. At 6 months, his FEV 1 was 49% and his diffusion capacity was 56%. He no longer required supplemental oxygen and now exercises daily.

Original languageEnglish (US)
Pages (from-to)e135-e137
JournalAnnals of Thoracic Surgery
Volume95
Issue number6
DOIs
StatePublished - Jun 1 2013

ASJC Scopus subject areas

  • Surgery
  • Pulmonary and Respiratory Medicine
  • Cardiology and Cardiovascular Medicine

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