Tracheal cartilaginous sleeve contributing to obstructive sleep apnea in a child with Crouzon syndrome

Seckin O. Ulualp, Steven T. Wright, Jean P. Font

Research output: Contribution to journalArticle

2 Citations (Scopus)

Abstract

Tracheal cartilaginous sleeve is characterized by the fusion of tracheal rings. Patients with tracheal cartilaginous sleeve may develop frequent respiratory tract infections, coughs, increased mucus production, sporadic cyanosis episodes, and failure to thrive due to alterations in the lower airway. Tracheal cartilaginous sleeve is seen exclusively in craniosynostosis. Craniosynostosis is described as the early fusion of skull sutures and causes abnormal development of the head. Crouzon syndrome is the most common syndromic craniosynostosis. Otolaryngologists may be asked to evaluate and manage breathing difficulties, sleep apnea, and hearing difficulties associated with Crouzon syndrome. Upper airway abnormalities such as hypertrophy of the tonsils and adenoids, midnasal stenosis, and choanal atresia have been reported. Lower airway abnormalities in the presence of obstructive airway symptoms have not been widely studied in Crouzon syndrome. We describe the diagnosis and management of multilevel airway problems in a child with Crouzon syndrome who presented with obstructive sleep apnea.

Original languageEnglish (US)
Pages (from-to)76-80
Number of pages5
JournalInternational Journal of Pediatric Otorhinolaryngology Extra
Volume1
Issue number1
DOIs
StatePublished - Mar 2006

Fingerprint

Craniofacial Dysostosis
Obstructive Sleep Apnea
Craniosynostoses
Choanal Atresia
Adenoids
Failure to Thrive
Cyanosis
Airway Management
Palatine Tonsil
Sleep Apnea Syndromes
Mucus
Cough
Skull
Respiratory Tract Infections
Hypertrophy
Sutures
Hearing
Pathologic Constriction
Respiration
Head

Keywords

  • Crouzon syndrome
  • Obstructive sleep apnea
  • Tracheal cartilaginous sleeve

ASJC Scopus subject areas

  • Otorhinolaryngology
  • Pediatrics, Perinatology, and Child Health

Cite this

Tracheal cartilaginous sleeve contributing to obstructive sleep apnea in a child with Crouzon syndrome. / Ulualp, Seckin O.; Wright, Steven T.; Font, Jean P.

In: International Journal of Pediatric Otorhinolaryngology Extra, Vol. 1, No. 1, 03.2006, p. 76-80.

Research output: Contribution to journalArticle

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