Cardiopulmonary Bypass Strategy for a Cyanotic Child with Hemoglobin SC Disease

Kelly A. Machovec, Robert D.B. Jaquiss, David D. Kaemmer, Warwick A. Ames, Hercilia M. Homi, Richard J. Walczak, Andrew J. Lodge, Edmund H. Jooste

Research output: Contribution to journalArticle

2 Citations (Scopus)

Abstract

Hemoglobin SC (HbSC) disease is a hemoglobinopathy that may produce sickling under conditions of hypoxemia, dehydration, and acidosis. We present a case of HbSC disease and tricuspid atresia, type IB. We describe management by cardiopulmonary bypass CPB using exchange transfusion at initiation of bypass and fractionation of collected blood, allowing platelet and plasma apheresis, as an option for patients unable to undergo this procedure off pump.

Original languageEnglish (US)
Pages (from-to)2373-2375
Number of pages3
JournalAnnals of Thoracic Surgery
Volume101
Issue number6
DOIs
StatePublished - Jun 1 2016

Fingerprint

Hemoglobin SC Disease
Cardiopulmonary Bypass
Tricuspid Atresia
Hemoglobinopathies
Blood Component Removal
Acidosis
Dehydration
Blood Platelets

ASJC Scopus subject areas

  • Surgery
  • Pulmonary and Respiratory Medicine
  • Cardiology and Cardiovascular Medicine

Cite this

Machovec, K. A., Jaquiss, R. D. B., Kaemmer, D. D., Ames, W. A., Homi, H. M., Walczak, R. J., ... Jooste, E. H. (2016). Cardiopulmonary Bypass Strategy for a Cyanotic Child with Hemoglobin SC Disease. Annals of Thoracic Surgery, 101(6), 2373-2375. https://doi.org/10.1016/j.athoracsur.2015.09.046

Cardiopulmonary Bypass Strategy for a Cyanotic Child with Hemoglobin SC Disease. / Machovec, Kelly A.; Jaquiss, Robert D.B.; Kaemmer, David D.; Ames, Warwick A.; Homi, Hercilia M.; Walczak, Richard J.; Lodge, Andrew J.; Jooste, Edmund H.

In: Annals of Thoracic Surgery, Vol. 101, No. 6, 01.06.2016, p. 2373-2375.

Research output: Contribution to journalArticle

Machovec, KA, Jaquiss, RDB, Kaemmer, DD, Ames, WA, Homi, HM, Walczak, RJ, Lodge, AJ & Jooste, EH 2016, 'Cardiopulmonary Bypass Strategy for a Cyanotic Child with Hemoglobin SC Disease', Annals of Thoracic Surgery, vol. 101, no. 6, pp. 2373-2375. https://doi.org/10.1016/j.athoracsur.2015.09.046
Machovec, Kelly A. ; Jaquiss, Robert D.B. ; Kaemmer, David D. ; Ames, Warwick A. ; Homi, Hercilia M. ; Walczak, Richard J. ; Lodge, Andrew J. ; Jooste, Edmund H. / Cardiopulmonary Bypass Strategy for a Cyanotic Child with Hemoglobin SC Disease. In: Annals of Thoracic Surgery. 2016 ; Vol. 101, No. 6. pp. 2373-2375.
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