Electrocardiographic characteristics of ventricular arrhythmia in inherited channelopathies

Ventricular arrhythmias in structurally normal hearts can be divided into idiopathic ventricular arrhythmia, in which there is no known ion mutation or genetic component, and inherited ion channelopathies, in which gene mutations causing ion-channel dysfunction play an important role in the mechanism of ventricular arrhythmia. Inherited channelopathies are Long QT syndrome, Short QT syndrome, Brugada syndrome, and catecholaminergic polymorphic ventricular tachycardia. Recognizing ECG patterns of these arrhythmias is important because they can cause sudden cardiac deaths that are preventable with defibrillator implantations.