Isolated infundibuloarterial inversion {S,D,I}: A newly recognized form of congenital heart disease

Ronald B. Foran, Christian Belcourt, Maurice A. Nanton, David A. Murphy, Arthur G. Weinberg, Jerome Liebman, Aldo R. Castañeda, Richard Van Praagh

Research output: Contribution to journalArticlepeer-review

23 Scopus citations

Abstract

A newly recognized form of congenital heart disease is presented that is characterized by visceroatrial situs solitus (S), D-loop ventricles (D), and inverted normally related great arteries (I). The segmental combination being {S,D,I}. This anomaly may be called isolated infundibuloarterial inversion because only the subsemilunar infundibulum and the great arteries are inverted, whereas the atria and the ventricles are not. All three patients had atrioventricular concordance, ventriculoatrial concordance, dextrocardia, superoinferior ventricles, crisscross atrioventricular relations, underdevelopment of the right ventricle, a large ventricular septal defect, and an inverted tetralogy of Fallot type of malformation of the infundibulum and great arteries. The condition known as crisscross atrioventricular relations was found in these three patients to be a major ventricular malposition characterized by marked clockwise rotation of the ventricles, as seen from the front. Two of these three cases were diagnosed accurately and repaired successfully.

Original languageEnglish (US)
Pages (from-to)1337-1350
Number of pages14
JournalAmerican Heart Journal
Volume116
Issue number5 PART 1
DOIs
StatePublished - Nov 1988

ASJC Scopus subject areas

  • Cardiology and Cardiovascular Medicine

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