Lethal mitochondrial cardiomyopathy in a hypomorphic Med30 mouse mutant is ameliorated by ketogenic diet

Philippe Krebs, Weiwei Fan, Yen Hui Chen, Kimimasa Tobita, Michael R. Downes, Malcolm R. Wood, Lei Sun, Xiaohong Li, Yu Xia, Ning Ding, Jason M. Spaeth, Eva Marie Y Moresco, Thomas G. Boyer, Cecilia Wen Ya Lo, Jeffrey Yen, Ronald M. Evans, Bruce Beutler

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Medicine & Life Sciences