Mechanism of hyperinsulinism in short-chain 3-hydroxyacyl-CoA dehydrogenase deficiency involves activation of glutamate dehydrogenase

Changhong Li, Pan Chen, Andrew Palladino, Srinivas Narayan, Laurie K. Russell, Samir Sayed, Guoxiang Xiong, Jie Chen, David Stokes, Yasmeen M. Butt, Patricia M. Jones, Heather W. Collins, Noam A. Cohen, Akiva S. Cohen, Itzhak Nissim, Thomas J. Smith, Arnold W. Strauss, Franz M. Matschinsky, Michael J. Bennett, Charles A. Stanley

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