Tricuspid atresia with absent pulmonary valve and intact ventricular septum: A rare association

Thomas H. Best, Himesh V. Vyas, Robert D B Jaquiss, Ritu Sachdeva

Research output: Contribution to journalArticle

4 Scopus citations

Abstract

The absence of the pulmonary valve in connection with tricuspid atresia and intact ventricular septum is a rare malformation, associated with a poor prognosis. The right ventricle is severely hypertrophied, resembling a cardiac mass protruding into the left ventricular outflow tract. We report such a case that underwent successful palliation with a Blalock-Taussig shunt followed by a superior cavopulmonary anastomosis.

Original languageEnglish (US)
Pages (from-to)393-396
Number of pages4
JournalCongenital Heart Disease
Volume6
Issue number4
DOIs
StatePublished - Jul 1 2011

Keywords

  • Absent pulmonary valve
  • Cardiac tumor
  • Left ventricular outflow obstruction
  • Right ventricular dysplasia
  • Three dimensional echocardiography
  • Tricuspid atresia

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health
  • Surgery
  • Radiology Nuclear Medicine and imaging
  • Cardiology and Cardiovascular Medicine

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